AtlasVesiculobullousErythema Multiforme

Vesiculobullous Diseases

Erythema Multiforme

aka EM · Erythema Multiforme Minor/Major

Acute, self-limiting mucocutaneous hypersensitivity reaction commonly triggered by HSV or drugs, with target lesions and haemorrhagic oral crusting.

Trigger
HSV (recurrent) / drugs
Skin
Target lesions
Course
Self-limiting 2-6 weeks

§ overviewOverview

Immune-mediated reaction pattern causing mucocutaneous blistering, often recurrent.

§ icdICD Classification

L51

§ etiologyEtiology

  • 01HSV (>70% of recurrent EM)
  • 02Mycoplasma pneumoniae
  • 03Drugs (sulfonamides, NSAIDs, anticonvulsants)

§ epidemiologyEpidemiology

Young adults (20–40). M > F.

§ pathogenesisPathogenesis

Cell-mediated immune response to viral antigens deposited in keratinocytes → apoptosis and blistering.

§ clinicalClinical Features

  • 01Oral: haemorrhagic crusting of lips, erosions on buccal/labial mucosa
  • 02Skin: target (iris) lesions — central vesicle, pale ring, erythematous halo
  • 03Acute onset, self-limiting 2–6 weeks
  • 04Recurrences common if HSV-associated

§ differentialDifferential Diagnosis

  • 01Pemphigus vulgaris
  • 02SJS/TEN
  • 03Primary herpes
  • 04Aphthous stomatitis

§ histopathHistopathology

  • 01Interface dermatitis
  • 02Keratinocyte apoptosis
  • 03Lymphocytic infiltrate at DEJ

§ investigationsInvestigations

  • 01Clinical diagnosis
  • 02Skin biopsy if atypical
  • 03HSV PCR if recurrent

§ classificationClassification

  • 01EM minor: skin ± oral, no systemic symptoms
  • 02EM major: more extensive, systemic symptoms
  • 03SJS/TEN: now considered separate spectrum

§ treatmentTreatment

  • 01Supportive: hydration, soft diet, analgesics
  • 02Topical steroids for oral lesions
  • 03Aciclovir prophylaxis for HSV-associated recurrent EM
  • 04Systemic steroids controversial

§ complicationsComplications

  • 01Dehydration
  • 02Secondary infection
  • 03Scarring (rare)

§ prognosisPrognosis

Excellent; self-limiting but may recur.

§ examKey Examination Points

  • 01Target lesions on skin
  • 02Haemorrhagic lip crusting
  • 03HSV is main trigger

§ revisionQuick Revision Summary

  • 01HSV trigger > drugs
  • 02Target lesions
  • 03Self-limiting 2-6 weeks

§ vivaBDS Viva Questions

  • 01What is the histology of EM?
  • 02Differentiate EM from SJS.
  • 03How do you prevent recurrence?

§ mcqsMCQs — Assessment (3)

Question 1

Most common trigger for recurrent EM:

Question 2

Characteristic skin lesion:

Question 3

Prevention of HSV-associated recurrent EM:

References

  1. Neville BW. Oral & Maxillofacial Pathology, 4e
  2. Scully C. Oral Medicine, 2e

Draft — pending faculty review. Educational use only; verify against current guidelines and primary sources before clinical application.